104. What is Lenegre’s disease or Lev’s disease?

Lenegre’s disease is idiopathic fibrosis of the cardiac conduction system resulting heart block. This most commonly occurs as a part of the ageing process of the heart in the elderly, however familial forms have been identified. Stokes-Adams attacks can be associated with Lenegre’s disease and result in syncope. Treatment is a permanent pacemaker depending on the rhythm that manifests.