Curbside Consultation of the Pancreas: 49 Clinical Questions

Scott Tenner, MD, MPH; Alphonso Brown, MD, MS Clin Epi; Frank Gress, MD

Question 44: Choledochal Cyst, What To Do? Watch, Ignore, Or Operate? (continued)

Yuriy Tsirlin, MD; Frank G. Gress, MD

Choledochal cysts are fairly rare findings of dilated extra- and/or intrahepatic sites. They are considered to be a disease of childhood and about 60% to 80% are diagnosed before the age of 10. However, at least 20% will go undiagnosed all the way into adulthood. The incidence of cystic dilatation of biliary ducts varies greatly among reports, anywhere from 1:100,000 to 150,000 to 1:2,000,000 with a female to male predominance of 3 to 4:1. The prevalence of this entity is higher in Eastern Asian countries, especially Japan; the reason for this discrepancy is unclear. No clear etiology for…